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Published by : PROFESSIONAL MEDICAL PUBLICATIONS |
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ISSN 1681-715X |
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ORIGINAL ARTICLE |
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Volume 26 |
January - March 2010 |
Number 1 |
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Gorlin-Goltz Syndrome
Atessa Pakfetrat1, Farnaz Falaki2,
Reza Zare Mahmoodabadi3, Shadi Saghafi4ABSTRACT
We report a case of Gorlin-Goltz syndrome in a 21-year-old man. Gorlin-Goltz syndrome (basal cell nevus syndrome) is an infrequent hereditary disease with its prevalence varying from 1/57,000 to 1/250,000.It is principally characterized by a wide range of developmental abnormalities. Main clinical manifestations include multiple odontogenic keratocysts of the jaws, facial basal cell carcinomas and skeletal anomalies. The prevalence varies from 1/57,000 to 1/250,000.
KEY WORDS
: Gorlin-Goltz Syndrome, Nevoid Basal Cell Carcinoma Syndrome (NBCCS), Basal Cell Nevus Syndrome, Odontogenic Keratocyst, Basal Cell Carcinoma.Pak J Med Sci January - March 2010 Vol. 26 No. 1 235-238
How to cite this article:
Pakfetrat A, Falaki F, Mahmoodabadi RZ, Saghafi S. Gorlin-Goltz Syndrome. Pak J Med Sci 2010;26(1):235-238
1. Atessa Pakfetrat,
Assistant Professor,
Department of Oral Medicine
2. Farnaz Falaki,
Assistant Professor,
Department of Oral Medicine
3. Reza Zare Mahmoodabadi,
Assistant Professor,
Department of Oral and Maxillofacial Pathology
4. Shadi Saghafi,
Assistant Professor,
Department of Oral and Maxillofacial Pathology
1-4: Faculty of Dentistry and Dental Research Center,
Mashhad University of Medical Sciences, Iran
Correspondence:
Farnaz Falaki,
E mail: falakif@mums.ac.ir
farnazfalaki@yahoo.com
* Received for Publication: November 17, 2009
* Accepted: January 2, 2010
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