Pakistan Journal of Medical Sciences

Published by : PROFESSIONAL MEDICAL PUBLICATIONS

ISSN 1681-715X

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REVIEW ARTICLE

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Volume 23

October - December 2007 (Part-I)

Number  5


 

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Adult onset stillís disease and prurigo pigmentosa:
An unusual association and review of literature

Tarek Abdel Hamed Mostafa Dowod1, M. El-Sayed Hanafy Khalel2, Magdy Abas Ali Mohammed3,
Maha Abdel Wahab Mohamed El Sharawy4, Sara Jassim Al-Ghabandi5, Anwaar Yahya Al-Sumait6

SUMMARY

This study was conducted in the Department of Medicine, Department of Dermatology, Al-Adan Hospital, Ministry of Health- Kuwait. This patient was hospitalized as a case of pyrexia of unknown origin. We report atypical skin eruption in this patient who fulfilled the criteria for Adult Onset Stillís Disease (AOSD) despite the absence of the typical stillís rash. Skin biopsy revealed prurigo pigmentosa (PP). To elucidate this unusual association, we searched the literature for the cutaneous manifestations of AOSD. Kahori T, et al had described PP like lesions in a patient with AOSD in addition to the typical stillís rash and it is the only case report that exists in English literature. In our case, except for stillís rash, all the criteria of AOSD were present, the diagnosis was made after excluding all other possible causes i.e. infectious diseases, other rheumatic diseases, vasculitis and malignant disease. The objective for reporting this case and review of literature is to shed more light on the rare dermatological disorder Prurigo Pigmentosa (PP) and its unusual association with Adult Onset Stillís Disease (AOSD).

Clinicians and dermatologist must be aware of this unusual association of PP and AOSD as the diagnosis of AOSD can be made in the absence of the typical stillís rash but in the presence of other atypical cutaneous manifestations including PP.

KEY WORDS: Prurigo pigmentosa, Adult Onset Stillís Disease, Stillís rash.

Abbreviations: Adult onset stillís disease (AOSD). Prurigo Pigmentosa (PP).

Pak J Med Sci    October - December 2007 (Part-I)    Vol. 23 No. 5    792-797


1. Tarek Abdel Hamed Mostafa Dowod,
Specialist, Dept. of Medicine,
2. Mohammed El-Sayed Hanafy Khalel,
Specialist, Dept. of Dermatology,
3. Magdy Abas Ali Mohammed,
Registrar, Dept. of Medicine,
4. Maha Abdel Wahab Mohamed El Sharawy,
Lecture of Pathology, Dept. of Pathology,
Ain Shames University, EGYPT.
5. Sara Jassim Al-Ghabandi,
Trainee, Dept. of Medicine,
6. Anwaar Yahya Al-Sumait
Trainee, Dept. of Medicine,
1-3,5,6: Al-Adan Hospital, Kuwait.

Correspondence

Dr. Tarek Abdel Hamed Mostafa Dowod,
Al-Adan Hospital, Ministry of Health,
Fahaheel, P.O Box: 47854, Kuwait.
E-mail: doriya70@hotmail.com

* Received for Publication: August 9, 2007
* Accepted: September 15, 2007



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